Pediatric ATI Practice Exam

Which lab value is important to monitor for a child with cystic fibrosis?

1. Blood glucose levels

2. Electrolyte levels

3. White blood cell count

4. Inability to clear secretions

The correct answer is: White blood cell count

In the context of cystic fibrosis, monitoring specific lab values is crucial as the condition affects multiple organ systems, particularly the lungs and digestive tract. While several values could be relevant in managing a child with cystic fibrosis, the most pertinent lab value to monitor is electrolyte levels. Children with cystic fibrosis often experience disruptions in electrolyte balance due to their condition, particularly involving sodium and chloride. The defective CFTR protein, associated with cystic fibrosis, leads to abnormal transport of these electrolytes, which can cause sweat with a higher salt content. This not only impacts hydration but can also affect the functioning of other organs, including the pancreas, where enzyme exchange is critical for digestion. Monitoring electrolyte levels helps in assessing the hydration status and ensuring proper dietary management, especially in hot weather or during illness when excessive sweating can lead to dehydration and potentially severe consequences. While blood glucose levels can be important to monitor, particularly as many individuals with cystic fibrosis develop diabetes, it is not as directly impacted by the core symptoms of the disease as electrolyte levels. White blood cell count can indicate infection, which is a concern in cystic fibrosis due to lung involvement, but it is not the primary lab value to monitor specifically related to the metabolic challenges presented by the disease. The